Home-Based Monitoring of Pulmonary Function in Patients with Duchenne Muscular Dystroph
نویسندگان
چکیده
منابع مشابه
Detection of the Duplication in Exons 56-63 of Duchenne Muscular Dystrophy Patients with MLPA
Background Duchenne Muscular Dystrophy (DMD) is a deadly X-linked recessive disorder. This genetic disorder affects 1 among 3,500-5,000 males in the world. The majority of the patients are male, due to the type of inheritance. It affects most of the skeletal, the respiratory, and cardiac muscles, causing these vital organs to contract and eventually mortality.<br...
متن کاملEffect of Home-based Pulmonary Rehabilitation on Daily Activity of Patients with Chronic Obstructive Pulmonary Disease
Background: Pulmonary rehabilitation is an important part of treatment in patients with COPD (Chronic Obstructive Pulmonary Disease) with the goal of achieving and maintaining maximum functional independence since this disease causes symptoms including fatigue, and consequently decrease in daily living activity. Aim: To determine the effect of home-based pulmonary rehabilitation on daily living...
متن کاملPrevention of pulmonary morbidity for patients with Duchenne muscular dystrophy.
STUDY OBJECTIVE To evaluate the effects of a new respiratory management protocol on respiratory morbidity and hospitalization rates for patients with Duchenne muscular dystrophy (DMD). DESIGN A retrospective cohort study. METHODS Using a protocol in which oxyhemoglobin desaturation was prevented or reversed by the use of noninvasive intermittent positive pressure ventilation (IPPV) and assi...
متن کاملCharacterization of pulmonary function in Duchenne Muscular Dystrophy
Decline in pulmonary function in Duchenne Muscular Dystrophy (DMD) contributes to significant morbidity and reduced longevity. Spirometry is a widely used and fairly easily performed technique to assess lung function, and in particular lung volume; however, the acceptability criteria from the American Thoracic Society (ATS) may be overly restrictive and inappropriate for patients with neuromusc...
متن کاملCharacterization of pulmonary function in 10–18 year old patients with Duchenne muscular dystrophy
Pulmonary function loss in patients with Duchenne muscular dystrophy (DMD) is progressive and leads to pulmonary insufficiency. The purpose of this study in 10-18 year old patients with DMD is the assessment of the inter-correlation between pulmonary function tests (PFTs), their reliability and the association with the general disease stage measured by the Brooke score. Dynamic PFTs (peak expir...
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ژورنال
عنوان ژورنال: Journal of Neuromuscular Diseases
سال: 2018
ISSN: 2214-3599,2214-3602
DOI: 10.3233/jnd-180338